Chapter 1. Orphan lung diseases: from definition to organisation of care.-Chapter 2. The challenge of clinical research in orphan diseases.- Chapter 3. Chronic bronchiolitis in adults.- Chapter 4. Allergic bronchopulmonary mycosis.- Chapter 5. Orphan tracheopathies.- Chapter 6. Amyloidosis of the lungs and airways.- Chapter 7. Eosinophilic granulomatosis with polyangiitis.- Chapter 8. Granulomatosis with polyangiitis.- Chapter 9. Alveolar hemorrhage.- Chapter 10. Pulmonary manifestations of large vessel vasculitis (Behçet and Takayasu disease) .- Chapter 11. Hepato-pulmonary syndrome.- Chapter 12. Systemic sclerosis and the lung.- Chapter 13. Rheumatoid arthritis and the lung.- Chapter 14. Lung disease in systemic lupus erythematosus, myositis, Sjögren disease and mixed connective tissue diseases.- Chapter 15. Interstitial pneumonia with autoimmune features, and overlap interstitial pneumonia.- Chapter 16. Non-Langerhans cell histiocytosis and the lung.- Chapter 17. Idiopathic eosinophilic pneumonias.- Chapter 18. Langerhans cell granulomatosis and smoking-related interstitial lung diseases.- Chapter 19. Lymphangioleiomyomatosis.- Chapter 20. Multiple cystic lung disease.- Chapter 21. Complex Thoracic Lymphatic Disorders of Adults.- Chapter 22. Pulmonary alveolar proteinosis.- Chapter 23. Gasteroesosophageal reflux, idiopathic pulmonary fibrosis and lung transplantation.- Chapter 24. Genetic and familial pulmonary fibrosis related to monogenic diseases.- Chapter 25. Diffuse bronchiectasis of genetic or idiopathic origin.- Chapter 26. Pulmonary vascular manifestations of hereditary hemorrhagic telangiectasia.- Chapter 27. Pulmonary alveolar microlithiasis.- Chapter 28. Rare diffuse lung diseases of genetic origin.- Chapter 29. Imaging approach to interstitial lung disease.- Chapter 30. Bronchoscopic approach to interstitial lung disease.- Chapter 31. An integrated approach to diagnosing interstitial lung disease.- Chapter 32. Idiopathic Pulmonary fibrosis and the many faces of UIP.- Chapter 33. Combined pulmonary fibrosis and emphysema (syndrome) .- Chapter 34. Nonspecific interstitial pneumonia, idiopathic or secondary.- Chapter 35. Organising pneumonias and acute interstitial pneumonia.- Chapter 36. Pleuro pulmonary fibroelastosis.- Chapter 37.Interstitial lung diseases of occupational origin.- Chapter 38. Unclassifiable Interstitital Lung Disease.- Chapter 39. Lymphoproliferative lung diseases.- Chapter 40. Pulmonary manifestations of hematological malignancies and recipients of bone marrow or stem cell transplantation.- Chapter 41. Pulmonary hypertension in orphan lung diseases.- Chapter 42. Drug-induced / iatrogenic respiratory disease: With emphasis on unusual, rare and emergent drug-induced reactions.- Chapter 43. Malignant mimics of orphan lung diseases.</p><p></p>